Amino acid formula with vitamins and minerals (msud, tyr, hcu coolers)
Brand: MSUD Cooler®, TYR Cooler®, HCU Cooler®
PBAC's latest decision on Amino acid formula with vitamins and minerals (msud, tyr, hcu coolers): Recommended (2018). Considered for Nutritional management of maple syrup urine disease (MSUD), tyrosinaemia (TYR), and homocystinuria (HCU) through provision of amino acids without specific branched-chain or other restricted amino acids.
PBAC outcome
Recommended
Restricted
ICER (AUD/QALY)
Not modelled
no economic evaluation
Submissions
1
first 2018
Submissions
1
2018 → 2018
Eligible population
Patients with maple syrup urine disease (MSUD), tyrosinaemia (TYR), and homocystinuria (HCU) requiring specialised amino acid nutrition.
Therapy area
Metabolic
Line of therapy
Not applicable
Evidence base
Cost-minimisation
Economic model
Cost-minimisation
ICER note
Not applicable — this is a minor submission for nutritional formulation changes with no economic evaluation.