Amino Acid Formula With Vitamins And Minerals (Msud, Tyr, Hcu Coolers)
Not recommended MetabolicRestrictedNot applicable line
Nutritional management of maple syrup urine disease (MSUD), tyrosinaemia (TYR), and homocystinuria (HCU) through provision of amino acids without specific branched-chain or other restricted amino acids.
1
Submissions
1 resub
2018–18
On the record
—
ICER range
Not modelled
Cost basis
Decision on record
- Meeting Nov 2011 Not recommended Medicinal food no PSD
Access path
- Mar 2018Recommended
- PBS listing · Restricted
RecommendedDeferredNot recommended
From the public summary
PBAC outcome
5.1 The PBAC noted the change to the listings processed by the secretariat. Outcome: RecommendedPSD · Mar 2018
Cost-effectiveness
Not applicable — this is a minor submission for nutritional formulation changes with no economic evaluation.
Decision context
PopulationPatients with maple syrup urine disease (MSUD), tyrosinaemia (TYR), and homocystinuria (HCU) requiring specialised amino acid nutrition.
Submission history
| Decided | Outcome | Comparator | ICER | Evidence |
|---|---|---|---|---|
| Mar 2018 | Recommended | — | — | Cost-minimisation |
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