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Amino Acid Formula With Fat, Carbohydrate Without Methionine

Recommended MetabolicRestricted benefitNot applicable line

dietary management of pyridoxine non-responsive homocystinuria (HCU)

1
Submissions
2019–19
On the record
—
ICER range
Cost-min
Cost basis

Decision on record

1 decision
  • Meeting Nov 2019 Recommended Pyridoxine non- responsive homocystinuria (HCU)

Access path

1 submission · public record
  1. Nov 2019
    Recommended · restricted

    vs HCU Cooler 20

  2. PBS listing · Restricted benefit
RecommendedDeferredNot recommended

From the public summary

Verbatim · PSD text · may span indications
PBAC outcome
7.1 The PBAC recommended the Restricted Benefit listing of amino acid formula with fat, carbohydrate without methionine, HCU Easy, for the dietary management of pyridoxine non-responsive homocystinuria (HCU).PSD · Nov 2019
7.2 The PBAC noted the NPWP supported the proposed listing as a treatment option for the dietary management of pyridoxine non-responsive HCU. The PBAC also noted the NPWP advice that HCU Easy does not contain any vitamins, minerals or trace elements, therefore patients would have to meet their dietary needs through other sources, which may include use of PBS-subsidised vitamin, mineral and trace element supplements such as Phlexy-vits and Paediatric …PSD · Nov 2019

Cost-effectiveness

Cost-minimisation analysis performed; no ICER calculated. Listing based on cost-equivalence per gram of protein equivalent to HCU Cooler 20.

Decision context

Populationpatients with pyridoxine non-responsive homocystinuria

Submission history

1 entries
DecidedOutcomeComparatorICEREvidence
Nov 2019 Recommended · restricted HCU Cooler 20 — cost-minimisation

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