Amino Acid Formula With Fat, Carbohydrate Without Methionine
Recommended MetabolicRestricted benefitNot applicable line
dietary management of pyridoxine non-responsive homocystinuria (HCU)
1
Submissions
2019–19
On the record
—
ICER range
Cost-min
Cost basis
Decision on record
- Meeting Nov 2019 Recommended Pyridoxine non- responsive homocystinuria (HCU)
Access path
- Nov 2019Recommended · restricted
vs HCU Cooler 20
- PBS listing · Restricted benefit
RecommendedDeferredNot recommended
From the public summary
PBAC outcome
7.1 The PBAC recommended the Restricted Benefit listing of amino acid formula with fat, carbohydrate without methionine, HCU Easy, for the dietary management of pyridoxine non-responsive homocystinuria (HCU).PSD · Nov 2019
7.2 The PBAC noted the NPWP supported the proposed listing as a treatment option for the dietary management of pyridoxine non-responsive HCU. The PBAC also noted the NPWP advice that HCU Easy does not contain any vitamins, minerals or trace elements, therefore patients would have to meet their dietary needs through other sources, which may include use of PBS-subsidised vitamin, mineral and trace element supplements such as Phlexy-vits and Paediatric …PSD · Nov 2019
Cost-effectiveness
Cost-minimisation analysis performed; no ICER calculated. Listing based on cost-equivalence per gram of protein equivalent to HCU Cooler 20.
Decision context
Populationpatients with pyridoxine non-responsive homocystinuria
Submission history
| Decided | Outcome | Comparator | ICER | Evidence |
|---|---|---|---|---|
| Nov 2019 | Recommended · restricted | HCU Cooler 20 | — | cost-minimisation |
Similar precedents
Amino Acid Formula With Vitamins And Minerals Without Methionine87%Amino Acid Formula With Vitamins And Minerals Without Methionine And Supplemented With Arachidonic Acid And Docosahexaenoic Acid83%Amino Acid Formula With Carbohydrate Without Phenylalanine70%Amino Acid Formula With Fat, Carbohydrate, Vitamins And Minerals Without Phenylalanine69%Betaine69%Amino Acid Formula With Vitamins And Minerals (Msud, Tyr, Hcu Coolers)69%Amino Acid Formula Without Phenylalanine67%Amino Acid Formula With Fat, Carbohydrate Without Phenylalanine And Tyrosine66%
Listed in law
PBS listings commencing 1 Jun 2020 were made by these 3 determinations under the National Health Act 1953. A determination covers every listing that commenced that day, so this is the legal instrument in force for the date — not a document naming this medicine. Open it and check.
| Determination | Made | Status | |
|---|---|---|---|
| PB 42 of 2020 | 29 May 2020 | Repealed | PDF ↗ |
| PB 43 of 2020 | 29 May 2020 | Repealed | PDF ↗ |
| PB 51 of 2020 | 29 May 2020 | Repealed | PDF ↗ |