Disease index

maple syrup urine disease

Metabolic · 2014–2023

6decisions
4medicines
0carried consumer input
0individual submissions

No submission for this condition has carried consumer input, including the 6 made since the comments facility came into use.

Every decision

MedicineMeetingOutcomeConsumer input
amino acid formula with vitamins and minerals without valine, leucine, isoleucine, supplemented with arachidonic acid and docosahexaenoic acid Dietary management of maple syrup urine disease (MSUD) in infants and young children from 6 months to 5 years of age. Mar 2023 Recommended with restriction none received
amino acid formula with fat, carbohydrate, without valine, leucine and isoleucine Dietary management of maple syrup urine disease (MSUD). Nov 2019 Recommended with restriction none received
amino acid formula with vitamins and minerals without valine, leucine and isoleucine Dietary management of patients with maple syrup urine disease (MSUD), specifically as a second-stage protein supplement for infants aged six months to five… Nov 2019 Recommended with restriction none received
Amino acid formula with vitamins and minerals (three formulations: without phenylalanine; without phenylalanine and tyrosine; without valine, leucine and isoleucine) Nutritional management of phenylketonuria (PKU), tyrosinaemia, and maple syrup urine disease (MSUD) in children. These are formulation upgrades (pack size… Mar 2015 Recommended no section in document
amino acid formula with vitamins and minerals without valine, leucine and isoleucine Treatment of maple syrup urine disease (MSUD). Jul 2014 Recommended with restriction no section in document
amino acid formula with vitamins and minerals without valine, leucine and isoleucine Nutritional formula for patients with maple syrup urine disease (MSUD) requiring amino acid supplementation without branched-chain amino acids. Nov 2014 Deferred no section in document

Conditions are classified by a language model from the indication text of each submission, so an individual label here can be wrong. Consumer input is read from the document's own consumer comments section: 0 of 6 decisions since 2014 carried some. Silence means no comment reached the committee through that facility, not that nobody was affected. More on how this was built.